Sinus venosus and unroofed coronary sinus defects: two cases diagnosed and treated in adulthood
نویسندگان
چکیده
منابع مشابه
Unroofed coronary sinus defect.
Subsequent echocardiogram showed a dilated right ventricle with moderate tricuspid regurgitation. There was pulmonary hypertension (estimated pulmonary arterial systolic pressure, 55 mm Hg). Transthoracic Doppler studies showed a left-to-right shunt with a shunt ratio of 2:1. However, the ductus arteriosus was not patent and there were no septal defects. The coronary sinus was dilated and there...
متن کاملTransesophageal Echocardiography for Coronary Sinus Imaging in Partially Unroofed Coronary Sinus
BACKGROUND Partially unroofed coronary sinus (PUCS) is a rare congenital cardiac anomaly and prone to be misdiagnosed. The purpose of this study was to explore the value of transesophageal echocardiography (TEE) in CS imaging for the detection of PUCS and to develop a special two-dimensional TEE-based en face view of CS. METHODS Twenty adult patients with suspected PUCS, showing a dilated cor...
متن کاملAnatomical repair of partially unroofed coronary sinus syndrome through the coronary sinus orifice.
A 15-year-old girl was admitted for repair of partially unroofed coronary sinus syndrome. A preoperative echocardiographic study disclosed the dilated coronary sinus and a draining blood flow into the right atrium from both the left atrium and the end of the coronary sinus. At surgery, the distal portion of the coronary sinus roof was found to be absent. The defect was repaired through the coro...
متن کاملUnroofed coronary sinus newly diagnosed in adult patients after corrected congenital heart disease
Patients with congenital heart disease corrected in early childhood may later in life present with cardiac symptoms caused by other associated congenital anomalies that were initially not diagnosed. Nowadays, several noninvasive imaging modalities are available for the visualisation of cardiac anatomy in great detail. We describe two patients with an unroofed coronary sinus, a rare congenital a...
متن کاملUnroofed coronary sinus in a patient with neurofibromatosis type 1
OBJECTIVE To report the uncommon association between neurofibromatosis type 1 (NF1) and unroofed coronary sinus. CASE DESCRIPTION Girl with four years and six months old who was hospitalized for heart surgery. The cardiac problem was discovered at four months of life. On physical examination, the patient presented several café-au-lait spots in the trunk and the limbs and freckling of the axil...
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ژورنال
عنوان ژورنال: Cardiovascular Medicine
سال: 2019
ISSN: 1664-204X
DOI: 10.4414/cvm.2019.02074